Defects of Secretion in Cystic Fibrosis

Outside Neurons/Inside Epithelia: Novel Activation of CFTR Cl? and HCO3 ? Conductances.- Role of CFTR and Other Ion Channels in Cystic Fibrosis.- Ion Channels in the Apical Membrane: Role of Electrical Coupling on Transepithelial Transport.- Ion Channels in Secretory Granules of the Pancreas: Molecular Identification and Their Role in Regulated Secretion.- Epithelial Transport and Intracellular Trafficking: Physiology and Pathophysiology.- Kinases, Cell Volume, and the Regulation of Chloride Channels.- The CLCAs: Proteins with Ion Channel, Cell Adhesion and Tumor Suppressor Functions.- Is Intervention in Inositol Phosphate Signaling a Useful Therapeutic Option for Cystic Fibrosis?.- An Inositol Phosphate Analog, INO-4995, Normalizes Electrophysiology in CF Airway Epithelia.- Vitamin C and Flavonoids Potentiate CFTR Cl Transport in Human Airway Epithelia.- Airway Glycoconjugates Secreted in Cystic Fibrosis and Severe Chronic Airway Inflammation Relationship with Pseudomonas aeruginosa.- Biosynthesis and Secretion of Mucins, Especially the MUC2 Mucin, in Relation to Cystic Fibrosis.