Introduction to Biliary Atresia

Masaki Nio, M.D., Ph.D., ACSF Masaki Nio is Professor and Chief of Pediatric Surgery at Tohoku University Graduate School of Medicine and Director of Pediatric Medical Center of Tohoku University Hospital. In 1981, he completed a M.D. course at Tohoku University School of Medicine. In 1983, he joined the Second Department of Surgery, Tohoku University Hospital, which Professor Morio Kasai presided over from 1963 to 1986. In 1987, he completed a Ph.D. course in Pediatric Surgery at Tohoku University Graduate School of Medicine. From 1991 to 1993, he worked as a research fellow in Children’s Hospital of Los Angeles, USA. He served as the President of Japanese Society of Pediatric Surgeons, a Board Member of Japan Surgical Society, a Board Member of Pacific Association of Pediatric Surgeons, the Chairman of Japanese Biliary Atresia Society, and so on. He has been a secretary general of Japanese Biliary Atresia Society since 2008.

Biliary Atresia: A Historical OverviewHistory of The Japanese Biliary Atresia Society (JABS)Japanese Biliary Atresia Registry (JBAR)Pathogenesis: OverviewPathogenesis: Genetics/EpigeneticsPathogenesis: Viral InfectionPathogenesis: Maternal MicrochimerismEpidemiology: Incidence and Gender RatioEpidemiology: Ethnic Variations/Family Histories/HeredityEpidemiology: Gestational Age/Birth Weight /Associated AnomaliesClassificationsMass Screening Stool Color Card SystemPrenatal Diagnosis and Signs/SymptomsIntracranial HemorrhagePathology Biomarkers Differential DiagnosisDiagnostic ModalitiesPreoperative Management and Direct CholangiographyOperative Procedures: Open Kasai ProcedureOperative Procedures: Laparoscopic Kasai ProcedureOperative Procedures: Re-do Kasai ProcedureOperative Procedures: Cadaveric Liver TransplantationOperative Procedures: Living Donor Liver TransplantationMedical Treatment: UDCA/SteroidMedical Treatment: Kampo MedicinePrevention/Treatment of Postoperative CholangitisNutritional SupportProtocols of Follow-up ManagementPrognostic IndicatorsLong-term Complications: Gastro-Esophageal VaricesLong-term Complications: HypersplenismLong-term Complications: Cholangitis/Gall StonesLong-term Complications: Hepatopulmonary SyndromeLong-term Complications: Portopulmonary HypertensionLong-term Complications: Liver Cirrhosis/Hepatic Encephalopathy Long-Term Results, GeneralLong-Term Results, Deformity of Intrahepatic Bile DuctsLong-Term Results, Social PerformanceLong-Term Results, Liver TransplantationBiliary Atresia and Pregnancy/DeliveryBiliary Atresia and MalignancyFuture ProspectsTransition in Biliary AtresiaSociety of Patients and FamiliesClinical Guidelines for Biliary Atresia