Hirschsprung's Disease and Allied Disorders (eBook)

Foreword 4
Preface 5
Contents 7
List of Contributors 12
Hirschsprung’s Disease: A Historical Perspective — 1691– 2005 15
Development of the Enteric Nervous System 27
Functional Anatomy of the Enteric Nervous System 35
Animal Models of Aganglionosis 64
The Molecular Genetics of Hirschsprung’s Disease 76
Normal Colonic Motor Function and Relevant Structure 92
Pathophysiology of Hirschsprung’s Disease 107
Hirschsprung’s Disease: Clinical Features 119
Congenital Anomalies and Genetic Associations in Hirschsprung’s Disease 126
Enterocolitis Complicating Hirschsprung’s Disease 143
Diagnosis of Hirschsprung’s Disease and Allied Disorders 154
Functional Diagnosis 161
Histopathological Diagnosis and Differential Diagnosis of Hirschsprung’s Disease 193
NADPH- Diaphorase Histochemistry 206
Immunohistochemical Studies 214
Electron Microscopic Studies of Hirschsprung’s Disease 228
Intestinal Neuronal Malformations ( IND): Clinical Experience and Treatment 236
Neurocristopathies and Particular Associations with Hirschsprung’s Disease 259
Megacystis- Microcolon- Intestinal Hypoperistalsis Syndrome 273
Degenerative Hollow Visceral Myopathy Mimicking Hirschsprung’s Disease 280
Adynamic Bowel Syndrome 292
Anal Sphincter Achalasia and Ultrashort Hirschsprung’s Disease 302
Laparoscopically Assisted Anorectal Pull- Through 328
Swenson’s Procedure 333
Soave’s Extramucosal Endorectal Pull- Through Procedure 340
Rehbein’s Procedure ( Deep Anterior Resection) 352
Chaptername Transanal Pull- Through for Hirschsprung’s Disease 362
Duhamel’s Procedure 368
Early and Late Complications Following Operative Repair of Hirschsprung’s Disease 377
Long- Term Results and Quality of Life After Treatment of Hirschsprung’s Disease and Allied Disorders 388
Subject Index 398