Paediatric Heart Disease

Piers Daubeney Consultant Paediatric and Fetal CardiologyRoyal Brompton, London, UK

Steven Webber Children's Hospital of Pittsburgh, PA, USA

M. Gatzoulis

K. Niwa

List of Contributors, ix
Preface, xi

Section I: General cardiology
1 Epidemiology and genetics, 1
Bradley B. Keller
2 Basic cardiac physiology, 6
Michael Cheung
3 Cardiac morphology and nomenclature, 11
S. Yen Ho

Section II: Clinical evaluation and investigation
4 History and clinical examination, 20
Lee Beerman
5 Basic non-invasive investigations, 26
Lee Beerman
6 Echocardiography and Doppler, 34
Michael L. Rigby
7 Diagnostic cardiac catheterization and angiography, 46
Michael L. Rigby
8 Advanced cardiac imaging, 54
Michael Cheung

Section III: Specifi c congenital heart lesions
Acyanotic lesions
9 Left-to-right shunts, 61
Phil Roberts
10 Right-sided malformations, 71
Victoria Jowett
11 Abnormalities of left ventricular infl ow and outfl ow, 79
Anna Seale
12 Aortic malformations, rings, and slings, 89
Alex Gooi
13 Coronary artery lesions, 97
Alex Gooi
Cyanotic lesions
14 Transposition and transposition complexes, 103
Georgios Giannakoulas and Michael A. Gatzoulis
15 Abnormalities of right ventricular outfl ow, 111
Michael L. Rigby
16 Common mixing situations, 124
Michael L. Rigby
Other lesions
17 Heterotaxy, scimitar, and arteriovenous malformations, 136
Michael L. Rigby

Section IV: Diseases of the peri-, endo- and myocardium
18 Pericardial disease and infectious endocarditis, 142
Michael Y. Henein and Koichiro Niwa
19 Cardiomyopathies and acute myocarditis, 150
Steven A. Webber and Brian Feingold
20 Cardiac tumors, 160
Koichiro Niwa and Shigeru Tateno

Section V: Pulmonary hypertension
21 Primary pulmonary arterial hypertension in children, 164
Alan G. Magee
22 Pulmonary arterial hypertension associated with congenital heart disease
(including Eisenmenger syndrome), 168
Mark S. Spence and Michael A. Gatzoulis

Section VI: Rhythm disorders
23 Bradyarrhythmias, 176
Jan Till
24 Tachyarrhythmias, 181
Jan Till

Section VII: Systemic disease with cardiovascular involvement
25 Rheumatic fever, 195
Maria Virginia Tavares Santana and Cleusa Cavalcanti Lapa Santos
26 Marfan syndrome and connective tissue disorders, 199
Koichiro Niwa and Shigeru Tateno
27 Kawasaki disease and Takayasu arteritis, 204
Koichiro Niwa and Shigeru Tateno
28 Hyperlipidemia, 209
Eric Quivers
29 Systemic hypertension, 214
Eric Quivers

Section VIII: Congenital heart disease at the extremes of life
30 Fetal cardiology, 222
Helena M. Gardiner
31 Adult congenital heart disease, 227
Anselm Uebing and Michael A. Gatzoulis

Section IX: Management strategies
32 Principles of medical management, 239
Zdenek Slavik
33 Catheter intervention, 246
Alan W. Nugent
34 Principles of surgical management, 252
Hideki Uemura
35 Heart, lung, and heart–lung transplantation, 257
Steven A. Webber

Section X: Common clinical problems in the office
36 Murmurs in asymptomatic patients, 265
William H. Neches and Gregory H. Tatum
37 Syncope and presyncope, 268
William H. Neches and Gregory H. Tatum
38 Chest pain, 270
William H. Neches and Gregory H. Tatum
39 Palpitations, 272
William H. Neches and Gregory H. Tatum
40 Stridor, 274
William H. Neches and Gregory H. Tatum
41 Cyanosis and cyanotic spells, 276
William H. Neches, Gregory H. Tatum, and Michael L. Rigby
42 Activity restriction, 280
William H. Neches and Gregory H. Tatum
Appendices
Appendix A Resuscitation algorithms, 282
Margarita Burmester
Appendix B Glossary of terms commonly used in pediatric cardiac disease, 287
Nick Hayes
Appendix C Pediatric cardiac drugs and dosages, 302
Sian Bentley
Appendix D Endocarditis prophylaxis, 317
Jamie Cheong
Appendix E Anticoagulation guidelines, 320
Sian Bentley and Alan G. Magee
Index, 324